Wang L L, Song Y T, Geng M Y, Mi Y F, Guo X Y, Wang L, Tang J F, Li Z, Li W C
Department of Otolaryngology Head and Neck Surgery, the Second Affiliated Hospital of Zhengzhou University, Zhengzhou, 450014, China.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2019 Mar;33(3):255-258. doi: 10.13201/j.issn.1001-1781.2019.03.017.
To further recognize the clinical characteristics of non-syndromic enlarged vestibular aqueduct through the retrospective analysis of cases, with the purpose of providing references for clinical diagnosis and treatment. Collect 54 cases of non-syndromic enlarged vestibular aqueduct, and analyze their clinical characteristics after history taking, physical examination, audiometry and imaging examination. Measure the biggest width of midpoint between internal and external of vestibular aqueduct on temporal bone thin-section CT, and analyze the relationship between the pipe width and sides of ear, types of hearing loss and degree of hearing loss through test. All 54 patients with non-syndromic enlarged vestibular aqueduct had bilateral ear involvement. There were 42 cases with prelingual deafness, 12 cases with postlingual deafness, and there were 38 ears with severe deafness, 70 ears with profound deafness. Ninety-six ears of hearing loss showed sensorineural deafness, and 12 ears manifested mixed deafness. The biggest width of midpoint between internal and external of vestibular aqueduct spread over 1.60-3.90 mm, and the average was 2.60 mm. There were no significant differences in data between left and right sides, degree of hearing loss and type of hearing loss. Non-syndromic enlarged vestibular aqueduct mainly manifests serious sensorineural deafness, and the diagnosis depends on imaging examination. There is no difference in the degree of expanding between left and right ear, and the extent of enlargement is not related to the type and the severity of hearing loss.
通过对病例的回顾性分析，进一步认识非综合征型大前庭导水管的临床特征，为临床诊断和治疗提供参考。收集54例非综合征型大前庭导水管患者，经病史采集、体格检查、听力测试及影像学检查后，分析其临床特征。在颞骨薄层CT上测量前庭导水管内外中点的最大宽度，通过检验分析管径与患耳侧别、听力损失类型及听力损失程度之间的关系。54例非综合征型大前庭导水管患者均为双耳受累。其中语前聋42例，语后聋12例，重度聋38耳，极重度聋70耳。听力损失96耳为感音神经性聋，12耳为混合性聋。前庭导水管内外中点的最大宽度为1.60～3.90mm，平均为2.60mm。左右侧别、听力损失程度及听力损失类型的数据差异无统计学意义。非综合征型大前庭导水管主要表现为严重的感音神经性聋，诊断依靠影像学检查。左右耳扩大程度无差异，扩大程度与听力损失类型及严重程度无关。
