Manjubashini D, Nagarajan K, Rajesh Kumar B
Department of Radiodiagnosis, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
Department of Pulmonary Medicine, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
Lung India. 2019 Mar-Apr;36(2):157-159. doi: 10.4103/lungindia.lungindia_122_18.
Pulmonary capillary hemangiomatosis (PCH) is a rare cause of primary pulmonary hypertension (PPH) diagnosed in children and young adults with a nonspecific clinical presentation of dyspnea, cough, chest pain, and fatigue. It is characterized by extensive proliferation of pulmonary capillaries within alveolar septa. The imaging features include diffuse centrilobular ground-glass opacities with features of pulmonary hypertension. We present a case of PCH in an 11-year-old boy who was diagnosed with PPH in echocardiography and referred for diagnostic imaging.
肺毛细血管血管瘤病(PCH)是儿童和年轻成人原发性肺动脉高压(PPH)的一种罕见病因,临床表现为呼吸困难、咳嗽、胸痛和疲劳等非特异性症状。其特征是肺泡间隔内肺毛细血管广泛增生。影像学表现包括弥漫性小叶中心性磨玻璃影及肺动脉高压征象。我们报告一例11岁男孩的PCH病例,该患儿经超声心动图诊断为PPH,并转诊接受诊断性影像学检查。