Ogawa A, Watanabe K
J Urol. 1986 Apr;135(4):755-7. doi: 10.1016/s0022-5347(17)45841-1.
We report on a boy with genitourinary neurofibromatosis. The patient presented with bilateral hydronephrosis, and a markedly enlarged penis and scrotum. Laparotomy showed a mass occupying the small pelvic cavity. Histologically, the mass was a plexiform neurofibroma. The enlarged genitalia seemed to be caused by involvement of neurofibromatosis. The patient underwent a successful ileal conduit diversion.
我们报告了一名患有泌尿生殖系统神经纤维瘤病的男孩。该患者表现为双侧肾积水,阴茎和阴囊明显增大。剖腹探查显示一个肿块占据了小盆腔。组织学检查显示,该肿块为丛状神经纤维瘤。生殖器增大似乎是由神经纤维瘤病累及所致。该患者成功接受了回肠代膀胱术。