Raza Farheen, Jehangir Maham, Nazir Rashed, Khan Nasir Aziz
Department of Radiology, Shifa International Hospital, Islamabad, Pakistan.
J Ayub Med Coll Abbottabad. 2019 Jan-Mar;31(1):136-137.
Megacystis microcolon intestinal hypoperistalsis syndrome also known as Berdon syndrome is characterized by enlarged urinary bladder, small colon and reduced or absent intestinal peristalsis. We report a case of 4 days old female suffering from MMIHS presenting with tension pneumoperitoneum. To the best of our knowledge, this is the first reported case of MMIHS, having this unusual presentation.
巨膀胱-小结肠-肠蠕动不良综合征（也称为伯登综合征）的特征是膀胱增大、结肠小以及肠蠕动减弱或消失。我们报告一例4日龄患巨膀胱-小结肠-肠蠕动不良综合征的女性患儿，表现为张力性气腹。据我们所知，这是首例报道的具有这种不寻常表现的巨膀胱-小结肠-肠蠕动不良综合征病例。
