Choi Jangyoun, Choi Hyuk Joon, Kang Kyo Joon, Kwon Ho, Shin Jongweon
Department of Plastic and Reconstructive Surgery, Uijeongbu St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Uijeongbu, Korea.
J Craniofac Surg. 2019 Sep;30(6):e521-e523. doi: 10.1097/SCS.0000000000005448.
Plexiform neurofibromas are common complications in neurofibromatosis type 1 patients. Currently, surgery is the treatment of choice. However, complete surgical resection is difficult due to the infiltration to the surrounding tissue and the increased vascularity. Plexiform neurofibromas arising in the orbito-temporal area pose a greater challenge due to its critical function and cosmetic importance of the face. Such plexiform neurofibromas, separately designated as orbito-temporal plexiform neurofibromas, show complex symptoms such as severe ptosis, ectropion, lacrimal gland dysfunction, and even vision loss. We present a case of successful correction of upper eyelid entropion and severe eyebrow ptosis in a 48-year-old orbito-temporal plexiform neurofibromas patient with combined forehead lift and blepharoplasty techniques including double fold formation and mass excision.
丛状神经纤维瘤是1型神经纤维瘤病患者的常见并发症。目前，手术是首选治疗方法。然而，由于肿瘤浸润周围组织且血管增多，完整的手术切除很困难。眶颞部出现的丛状神经纤维瘤因其对面部重要功能和美观的影响而带来更大挑战。这种丛状神经纤维瘤，被单独命名为眶颞部丛状神经纤维瘤，表现出复杂的症状，如严重上睑下垂、睑外翻、泪腺功能障碍，甚至视力丧失。我们报告了一例48岁眶颞部丛状神经纤维瘤患者，采用前额提升术和眼睑成形术相结合的技术，包括双眼皮形成和肿物切除，成功矫正上睑内翻和严重眉下垂的病例。
