Ruzzini Laura, Donati Fabrizio, Russo Rosa, Costici Pier Francesco
Department of Orthopaedics, Children's Hospital "Bambino Gesù," Rome, Italy.
Indian J Orthop. 2019 Jan-Feb;53(1):122-127. doi: 10.4103/ortho.IJOrtho_505_17.
Patellar instability is a common problem in Down syndrome patients since their childhood. Several treatment have been proposed, but relapses are frequent and not all surgeries are suitable for growing patients. The aim of the present study is to evaluate the clinical and radiographic outcomes of a modified Roux-Goldthwait technique, for the management of patellar instability in children with Down syndrome at minimum 5-year followup.
19 patients (23 knees) affected by Down syndrome surgically treated for patellar dislocation, between 2000 and 2012 were included in this study. The mean age of patients was 9.5 years (range 3.7 - 15 years) and had a Dugdale Grade III, IV, and V patellar dislocation. Trochlear groove dysplasia was present in 15 patients. Each patient was clinically evaluated considering relapse rate, pre- and postoperative range of motion (ROM), Kujala score, and modified Lysholm score. Radiographic examination was performed on standard X-ray considering patellar height, trochlear angle, and patellofemoral congruence angle.
The mean followup was 134 months (range 62-206 months). No case of relapse of dislocation was registered with an improved ROM (significant for knee extension, < 0.05). The Kujala score showed significant improvement from a mean preoperative value of 39 ± 6.3 to a mean postoperative value of 92.7 ± 3.4 ( < 0.05) at final followup such as the modified Lysholm score (from mean preoperative 55.6 ± 6.3 to mean postoperative of 94.2 ± 2.6). Radiographs performed at latest followup showed a tendency to normalization of all the parameters considered, with a restored patellofemoral congruence and trochlear groove shape and without signs of osteoarthritis.
The present study showed that the Roux-Goldthwait procedure is a valid surgical option for the treatment of patellar dislocation in children with Down syndrome.
髌股关节不稳定是唐氏综合征患者自幼就有的常见问题。已经提出了几种治疗方法,但复发频繁,并非所有手术都适用于正在生长发育的患者。本研究的目的是评估改良Roux-Goldthwait技术在至少5年随访期内治疗唐氏综合征儿童髌股关节不稳定的临床和影像学结果。
本研究纳入了2000年至2012年间因髌股关节脱位接受手术治疗的19例(23膝)唐氏综合征患者。患者的平均年龄为9.5岁(范围3.7 - 15岁),均为Dugdale III级、IV级和V级髌股关节脱位。15例患者存在滑车沟发育不良。对每位患者进行临床评估,包括复发率、术前和术后活动范围(ROM)、Kujala评分和改良Lysholm评分。采用标准X线片进行影像学检查,测量髌骨高度、滑车角和髌股关节适合角。
平均随访时间为134个月(范围62 - 206个月)。未出现脱位复发病例,ROM有所改善(膝关节伸展角度改善显著,P < 0.05)。最终随访时,Kujala评分从术前平均39 ± 6.3显著提高至术后平均92.7 ± 3.4(P < 0.05),改良Lysholm评分也从术前平均55.6 ± 6.3提高至术后平均94.2 ± 2.6。最近一次随访时的X线片显示,所有测量参数均有恢复正常的趋势,髌股关节适合度和滑车沟形态恢复正常,且无骨关节炎迹象。
本研究表明,Roux-Goldthwait手术是治疗唐氏综合征儿童髌股关节脱位的一种有效手术选择。