Clinic for General and Interventional Cardiology/Angiology, Herz- und Diabeteszentrum NRW, Ruhr-Universität Bochum, Bad Oeynhausen, Germany.
Unidade de Genética, Departamento de Patologia, Faculdade de Medicina, Universidade do Porto, Alameda Hernâni Monteiro, 4200-319, Porto, Portugal; i3S -Instituto de Investigação e Inovação em Saúde, Universidade do Porto, 4200-135, Porto, Portugal.
Mol Cell Probes. 2019 Jun;45:79-83. doi: 10.1016/j.mcp.2019.03.008. Epub 2019 Mar 29.
Monogenetic diseases can be analyzed routinely by targeted DNA sequencing. If causative variants are not found, complementary methods like RNA sequencing or analysis of copy number variations by multiplex ligation-dependent probe amplification have to be considered. In the latter, especially exonic duplications or deletions can be detected, but the precise sites of mutations remain unclear. As we demonstrate in this casuistic report of Fabry disease, next-generation sequencing (NGS) of a long-range PCR product can identify the recombination site directly and illuminate the underlying molecular mechanism.
单基因疾病可通过靶向 DNA 测序进行常规分析。如果未发现致病变异,则需要考虑互补方法,如 RNA 测序或多重连接依赖性探针扩增分析拷贝数变异。在后一种方法中,可以检测到特别是外显子重复或缺失,但突变的确切部位仍不清楚。正如我们在这个法布里病的病例报告中所展示的那样,长距离 PCR 产物的下一代测序 (NGS) 可以直接识别重组位点,并阐明潜在的分子机制。