Wilson disease: Clinical manifestations, diagnosis, and treatment.
作者信息
Schilsky Michael L
机构信息
Departments of Medicine and Surgery Yale University Medical Center 333 Cedar Street New Haven CT.
出版信息
Clin Liver Dis (Hoboken). 2014 May 27;3(5):104-107. doi: 10.1002/cld.349. eCollection 2014 May.
Abstract
摘要
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本文引用的文献
1
Psychiatric aspects of Wilson disease: a review.Wilson 病的精神科方面：综述。
Gen Hosp Psychiatry. 2014 Jan-Feb;36(1):53-62. doi: 10.1016/j.genhosppsych.2013.08.007. Epub 2013 Oct 9.
2
Long-term outcomes of patients with Wilson disease in a large Austrian cohort.一项大型奥地利队列研究中 Wilson 病患者的长期结局。
Clin Gastroenterol Hepatol. 2014 Apr;12(4):683-9. doi: 10.1016/j.cgh.2013.09.025. Epub 2013 Sep 25.
3
EASL Clinical Practice Guidelines: Wilson's disease.EASL 临床实践指南：肝豆状核变性。
J Hepatol. 2012 Mar;56(3):671-85. doi: 10.1016/j.jhep.2011.11.007.
4
Wilson disease: pathogenesis and clinical considerations in diagnosis and treatment.威尔逊病：发病机制及诊断与治疗中的临床相关问题
Semin Liver Dis. 2011 Aug;31(3):245-59. doi: 10.1055/s-0031-1286056. Epub 2011 Sep 7.
5
Zinc monotherapy is not as effective as chelating agents in treatment of Wilson disease.锌剂单独治疗对于威尔逊病的疗效不如螯合剂。
Gastroenterology. 2011 Apr;140(4):1189-1198.e1. doi: 10.1053/j.gastro.2010.12.034. Epub 2010 Dec 24.
6
Liver transplantation for children with Wilson disease: comparison of outcomes between children and adults.儿童肝移植治疗肝豆状核变性：儿童与成人结局比较。
Clin Transplant. 2011 Jan-Feb;25(1):E52-60. doi: 10.1111/j.1399-0012.2010.01327.x. Epub 2010 Oct 14.
7
Screening for Wilson disease in acute liver failure: a comparison of currently available diagnostic tests.急性肝衰竭中威尔逊病的筛查：现有诊断试验的比较
Hepatology. 2008 Oct;48(4):1167-74. doi: 10.1002/hep.22446.
8
Diagnosis and treatment of Wilson disease: an update.威尔逊病的诊断与治疗：最新进展
Hepatology. 2008 Jun;47(6):2089-111. doi: 10.1002/hep.22261.
9
Treatment of Wilson disease with ammonium tetrathiomolybdate: IV. Comparison of tetrathiomolybdate and trientine in a double-blind study of treatment of the neurologic presentation of Wilson disease.用四硫代钼酸铵治疗肝豆状核变性：IV. 在肝豆状核变性神经系统表现治疗的双盲研究中四硫代钼酸铵与曲恩汀的比较
Arch Neurol. 2006 Apr;63(4):521-7. doi: 10.1001/archneur.63.4.521.
10
Wilson's disease in children: 37-year experience and revised King's score for liver transplantation.儿童威尔逊病：37年经验及肝移植修订版国王评分
Liver Transpl. 2005 Apr;11(4):441-8. doi: 10.1002/lt.20352.
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