Department of Pathology, Peking University First Hospital, Beijing 100034, P.R. China.
Department of Pathology, Peking University Health Science Center, Beijing 100191, P.R. China.
Oncol Rep. 2019 Jun;41(6):3219-3232. doi: 10.3892/or.2019.7112. Epub 2019 Apr 12.
The inactivation of tumor suppressor gene positive regulatory domain containing I (PRDM1) and activation of signal transducer and activator of transcription 3 (STAT3) have been detected in the majority of extranodal NK/T‑cell lymphoma, nasal type (EN‑NK/T‑NT) cases. In the present study, their association with and effects on the clinicopathologic features of EN‑NK/T‑NT are described. PRDM1 was revealed to be expressed in 19 out of 58 patients (32.8%) with EN‑NK/T‑NT, and phosphorylated STAT3 was overexpressed in 42 out of 58 (72.4%). Oncogenic pathways were investigated by NanoString encounter technology in 5 PRDM1(+) and 5 PRDM1(‑) EN‑NK/T‑NT specimens. Multiple oncogenic pathways involved in cell apoptosis, cellcycle (CC) and angiogenesis were discriminately activated in EN‑NK/T‑NT cases, and in PRDM1(+) cases in particular. The sustained activation of the Janus kinase 3 (JAK)/STAT3 pathway was more pronounced. In addition, missense mutations in the SRC homology 2 domain of STAT3 were detected in 7 out of 37 EN‑NK/T‑NT cases (18.92%), and the acquired mutation was related to the activation of the JAK3/STAT3 pathway. The downregulation of PRDM1 and upregulation of phospho‑STAT3 (Tyr705) were associated with angiocentric infiltration of EN‑NK/T‑NT (P=0.039). Notably, the prognosis of patients in the PRDM1(+)/STAT3 [mutated (mut‑)] group was considerably improved than that of patients in the STAT3(mut+)/PRDM(‑) group (P=0.037). In addition, the inhibition of NK/T cell lymphoma cell lines by Stattic and tofacitinib could suppress cell proliferation by inducing cell apoptosis or arresting the CC. The present results revealed that the JAK3/STAT3 oncogenic pathway and PRDM1 expression could stratify clinicopathologic features of EN‑NK/T‑NT. The inhibition of the JAK3/STAT3 pathway may serve as a treatment option for EN‑NK/T‑NT.
肿瘤抑制基因阳性调节域包含 I(PRDM1)的失活和信号转导子和转录激活因子 3(STAT3)的激活已在大多数结外 NK/T 细胞淋巴瘤,鼻型(EN-NK/T-NT)病例中检测到。在本研究中,描述了它们与 EN-NK/T-NT 的临床病理特征的关联及其对其的影响。PRDM1 在 58 例 EN-NK/T-NT 患者中的 19 例(32.8%)中表达,磷酸化 STAT3 在 58 例中的 42 例(72.4%)中过表达。通过 NanoString 遭遇技术在 5 例 PRDM1(+)和 5 例 PRDM1(-)EN-NK/T-NT 标本中研究致癌途径。细胞凋亡、细胞周期(CC)和血管生成的多个致癌途径在 EN-NK/T-NT 病例中被特异性激活,特别是在 PRDM1(+)病例中。Janus 激酶 3(JAK)/STAT3 通路的持续激活更为明显。此外,在 37 例 EN-NK/T-NT 病例中的 7 例(18.92%)中检测到 STAT3 的 SRC 同源 2 结构域的错义突变,获得的突变与 JAK3/STAT3 通路的激活有关。PRDM1 的下调和磷酸化 STAT3(Tyr705)的上调与 EN-NK/T-NT 的血管中心浸润有关(P=0.039)。值得注意的是,PRDM1(+)/STAT3 [突变(mut-)]组患者的预后明显优于 STAT3(mut+)/PRDM(-)组患者(P=0.037)。此外,Stattic 和托法替尼对 NK/T 细胞淋巴瘤细胞系的抑制可通过诱导细胞凋亡或阻止 CC 来抑制细胞增殖。本研究结果表明,JAK3/STAT3 致癌通路和 PRDM1 表达可分层 EN-NK/T-NT 的临床病理特征。抑制 JAK3/STAT3 通路可能成为治疗 EN-NK/T-NT 的一种选择。