John Ann M, Francisco Gina, Srivastava Radhika, Bhatti Hamza, Rao Babar K
Department of Dermatology, Rutgers Robert Wood Johnson Medical School, Somerset, NJ, USA.
Department of Dermatology, Weill Cornell Medical College, New York, NY, USA.
SAGE Open Med Case Rep. 2019 Apr 28;7:2050313X19847785. doi: 10.1177/2050313X19847785. eCollection 2019.
Dermatofibrosarcoma protuberans is an uncommon low-grade malignant tumor that can invade locally and rarely metastasize. Dermatofibrosarcoma protuberans has a high rate of local recurrence due to incomplete excision, especially in deep tissues. Morbidity is often related to multiple local recurrences and removal of excessive tissue with large, complex repairs. We present a case of incompletely excised dermatofibrosarcoma protuberans after initial wide local excision. We subsequently employed a "deep" vertical Mohs micrographic surgical technique to remove the remaining tumor while creating a flap with the tumor-free superficial portion to preserve tissue and avoid a complicated repair. The patient is tumor-free for 7 years.
隆突性皮肤纤维肉瘤是一种罕见的低度恶性肿瘤,可局部浸润,很少发生转移。由于切除不完全,尤其是在深部组织中,隆突性皮肤纤维肉瘤的局部复发率很高。发病率通常与多次局部复发以及因大面积复杂修复而切除过多组织有关。我们报告一例初次广泛局部切除后隆突性皮肤纤维肉瘤切除不完全的病例。随后,我们采用“深部”垂直莫氏显微外科技术切除剩余肿瘤,同时用无肿瘤的浅表部分制作皮瓣,以保留组织并避免复杂的修复。该患者已无瘤生存7年。