Withybush General Hospital, Haverfordwest, UK
Withybush General Hospital, Haverfordwest, UK.
Clin Med (Lond). 2019 May;19(3):250-251. doi: 10.7861/clinmedicine.19-3-250.
Hepatopulmonary syndrome (HPS) is often not considered as a cause of breathlessness in patients with liver cirrhosis. It consists of a triad of liver disease, intrapulmonary shunting and hypoxaemia. Here we discuss HPS in a patient presenting with acute on chronic breathlessness and typical features of orthodeoxia and platypnoea. Evidence of intrapulmonary shunting on imaging was essential to making the diagnosis, which carries a poor prognosis and was an urgent indication for liver transplantation.
肝肺综合征(HPS)常不被认为是肝硬化患者呼吸困难的原因。它由肝病、肺内分流和低氧血症组成。在这里,我们讨论了一位表现为急性加重慢性呼吸困难和典型的低氧血症和仰卧呼吸急促特征的患者的 HPS。影像学上存在肺内分流的证据对诊断至关重要,该疾病预后不良,是肝移植的紧急指征。