Cossa Matchecane, Robinson Tyler D
Departmento de Cirurgia, Hospital Central de Maputo, Maputo, Mozambique; Ministério de Saúde de Moçambique, Maputo, Mozambique.
Albany Medical Center, Albany, New York, USA.
Int J Surg Case Rep. 2019;60:49-52. doi: 10.1016/j.ijscr.2019.05.049. Epub 2019 Jun 5.
Intrapericardial congenital diaphragmatic hernia (IPCDH) is extremely rare: only 18 cases in children have been reported in the literature since 1981. We report the 19th case of infantile IPCDH in a 6-month-old girl and compare with previous reports.
Our patient initially presented with four days of dyspnea and was diagnosed with CDH by preoperative radiography. She was taken to the operating room, where an IPCDH was discovered, and successfully reduced.
CDH may present with cardiopulmonary compromise, but IPCDH directly compress the heart, leading to acute or subacute heart failure.
Pediatric surgeons should be aware of and prepared for the possibility of IPCDH when making surgical plans to correct CDH.
心包内先天性膈疝(IPCDH)极为罕见:自1981年以来,文献中仅报道了18例儿童病例。我们报告了一名6个月大女孩的第19例婴儿IPCDH病例,并与先前的报告进行比较。
我们的患者最初因呼吸困难4天就诊,术前影像学检查诊断为先天性膈疝(CDH)。她被送往手术室,在那里发现了IPCDH,并成功复位。
CDH可能表现为心肺功能不全,但IPCDH直接压迫心脏,导致急性或亚急性心力衰竭。
小儿外科医生在制定纠正CDH的手术计划时,应意识到IPCDH的可能性并做好准备。