[颅眶神经纤维瘤病。附病例报告]
[Cranio-orbital neurofibromatosis. Apropos of a case].
作者信息
Slama M, Princ G, Grob R, Boumendjel S, Vaillant J M
机构信息
Hôpital de la Salpêtrière, Paris.
出版信息
Rev Stomatol Chir Maxillofac. 1987;88(4):235-9.
Principal general manifestations of Recklinghausen's disease are outlined, with emphasis on cephalic lesions, particularly cranio-orbital localizations responsible in a large number of cases for lysis of greater wing of sphenoid. This is associated, amongst other complications, with ophthalmologic sequelae. A clinical case is presented, allowing discussion of the two essential problems raised by cranio-orbital neurofibromatosis: 1) conservation or not of the eye during necessary surgical treatment and 2) the course of the disease which is always progressive.
本文概述了神经纤维瘤病的主要一般表现，重点关注头部病变，尤其是颅眶部病变，在大量病例中这些病变导致蝶骨大翼骨质溶解。这与其他并发症一起，还伴有眼科后遗症。本文介绍了一个临床病例，以讨论颅眶部神经纤维瘤病引发的两个基本问题：1）在必要的手术治疗期间是否保留眼球；2）疾病的进程，其总是呈进行性发展。
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