El-Doueihi Robert Zakhia, Salti Ibrahim, Maroun-Aouad Marie, El Hajj Albert
Department of Surgery, American University of Beirut-MC, Beirut, Lebanon.
Department of Internal Medicine, American University of Beirut-MC, Beirut, Lebanon.
Urol Case Rep. 2019 Mar 22;24:100876. doi: 10.1016/j.eucr.2019.100876. eCollection 2019 May.
Pheochromocytoma is a sympathetic paraganglioma originating from the chromaffin cells. They are bilateral in 10% of cases and occur as a part of a MEN 2A or 2B syndromes. This is a case of bilateral asymptomatic pheochromocytomas diagnosed incidentally on imaging in a woman being investigated for secondary infertility. Laboratory tests were negative. Whole body FDG scan showed avid uptake of the tracer by both adrenal masses, but none in the thyroid. Hypertensive crisis occurred during right adrenalectomy on an unprepared patient in spite of clamping the adrenal vein, which raises the need for alpha-adrenergic blockade for patients undergoing adrenalectomy.
嗜铬细胞瘤是一种起源于嗜铬细胞的交感神经节细胞瘤。10%的病例为双侧性,且可作为2A或2B型多发性内分泌腺瘤综合征的一部分出现。这是一例双侧无症状嗜铬细胞瘤的病例,在一名因继发性不孕接受检查的女性患者的影像学检查中偶然发现。实验室检查结果为阴性。全身FDG扫描显示,双侧肾上腺肿块均有放射性示踪剂摄取,但甲状腺未见摄取。尽管在右肾上腺切除术中钳夹了肾上腺静脉,但一名未做准备的患者仍发生了高血压危象,这凸显了对接受肾上腺切除术的患者进行α-肾上腺素能阻滞的必要性。