Kamoun Salma, Azouz Heifa, Zemmali Marwa, Haouet Slim, Kchir Nidhameddine
Department of Pathology, Rabta Hospital, Faculty of Medicine of Tunis, University of Tunis el Manar, Tunisia.
Department of Neurosurgery, National Institute of Neurology, Tunis, Tunisia.
Pan Afr Med J. 2019 Mar 11;32:113. doi: 10.11604/pamj.2019.32.113.12669. eCollection 2019.
The term desmoplastic infantile ganglioglioma was coined by VandenBerg et al in 1987. In their first report these authors referred to a rare, distinct brain tumor. About 60 cases of desmoplastic infantile ganglioglioma have been described in the literature since its first description. We report a case of a 6-year-old girl who was admitted for seizure without family history. Magnetic resonance imaging scan showed a hypodense area in the right temporal region. A right temporal craniotomy was performed and the tumor was excised. The pathologic examination revealed the diagnosis of desmoplastic infantile ganglioglioma.
促纤维增生性婴儿型神经节胶质瘤这一术语由范登伯格等人于1987年提出。在他们的首次报告中,这些作者提到了一种罕见的、独特的脑肿瘤。自首次描述以来,文献中已报道了约60例促纤维增生性婴儿型神经节胶质瘤病例。我们报告一例6岁女童,因癫痫发作入院,无家族病史。磁共振成像扫描显示右侧颞叶区域有一个低密度区。进行了右侧颞叶开颅手术并切除了肿瘤。病理检查确诊为促纤维增生性婴儿型神经节胶质瘤。