Doan Tam T, Wang Alicia, Davey Brooke, Upadhyay Shailendra, Toro-Salazar Olga
The Lillie Frank Abercrombie Section of Cardiology, Department of Pediatrics, Texas Children's Hospital, Baylor College of Medicine, 6651 Main Street. Legacy Tower, E1920, Houston, TX, 77030-2303, USA.
Department of Pediatric Cardiology, Connecticut Children's Medical Center and University of Connecticut School of Medicine, Hartford, CT, 06106, USA.
Pediatr Cardiol. 2019 Dec;40(8):1748-1751. doi: 10.1007/s00246-019-02141-z. Epub 2019 Jun 24.
We report two cases of prenatally diagnosed double aortic arch with dominant right arch and a left-sided ductus arteriosus, consistent with a complete vascular ring. Postnatal transthoracic echocardiogram and cardiac magnetic resonance imaging demonstrated a spontaneous closure of the ductus arteriosus and obliteration of the left aortic arch distal to the origin of the left subclavian artery in both cases. Spontaneous closure of the ductus arteriosus involving extended ductal tissue in the left aortic arch likely led to obliteration of the distal left arch after birth. One patient presented with recurrent symptoms suggestive of dysphagia and underwent a successful surgical repair of the vascular ring with resolution of symptoms. The other patient has been asymptomatic and is 4 years old at the time of this report.
我们报告两例产前诊断为双主动脉弓且右弓占优势、左侧动脉导管未闭的病例，符合完全性血管环。产后经胸超声心动图和心脏磁共振成像显示，两例患者的动脉导管均自发闭合，左锁骨下动脉起源远端的左主动脉弓闭塞。左主动脉弓中累及延伸导管组织的动脉导管自发闭合，可能导致出生后左弓远端闭塞。一名患者出现反复提示吞咽困难的症状，接受了血管环的成功手术修复，症状得以缓解。另一例患者无症状，在撰写本报告时为4岁。
