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闭锁性异常左锁骨下动脉作为一种罕见血管环的一部分。

Atretic anomalous left subclavian artery as part of an unusual vascular ring.

作者信息

Powell Shannon K, Patel Jyoti K, Ebenroth Eric S

机构信息

Department of Pediatric Cardiology,Indiana University School of Medicine,Indianapolis,IN,USA.

出版信息

Cardiol Young. 2019 Jan;29(1):85-87. doi: 10.1017/S1047951118001737. Epub 2018 Oct 26.

DOI:10.1017/S1047951118001737
PMID:30360770
Abstract

In this report, a unique case of a symptomatic vascular ring formed by right aortic arch, aberrant left subclavian artery, and left ligamentum arteriosus in which there is atresia of the proximal left subclavian artery is described. Imaging modalities were non-diagnostic and the patient was sent to surgery based on strong clinical suspicion. Her anatomy was delineated in the operating room and the ring was successfully repaired.

摘要

在本报告中,描述了一例由右主动脉弓、异常左锁骨下动脉和左动脉韧带形成的有症状血管环的独特病例,其中左锁骨下动脉近端闭锁。影像学检查未能明确诊断,基于强烈的临床怀疑,患者被送去接受手术。在手术室中明确了其解剖结构,血管环修复成功。

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引用本文的文献

1
Relationship Between Quantitative Tracheal Geometry and Clinical Course in Various Types of Vascular Ring.不同类型血管环中气管定量几何形态与临床病程的关系
Pediatr Cardiol. 2024 Aug 12. doi: 10.1007/s00246-024-03617-3.
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Subclavian steal syndrome in a right aortic arch with aberrant left subclavian artery atresia.右主动脉弓伴左锁骨下动脉闭锁异常时的锁骨下动脉盗血综合征。
SAGE Open Med Case Rep. 2023 Jun 16;11:2050313X231179305. doi: 10.1177/2050313X231179305. eCollection 2023.
3
Subclavian Steal Phenomenon Associated With Vascular Ring in an Infant Who Had a Prenatally Diagnosed Right Aortic Arch With an Atretic Aberrant Left Subclavian Artery.
与血管环相关的锁骨下动脉窃血现象出现在一名婴儿中,该婴儿在产前被诊断为右主动脉弓伴左锁骨下动脉闭锁性迷走。
Tex Heart Inst J. 2022 Sep 1;49(5). doi: 10.14503/THIJ-20-7415.