Moebius 综合征：牙科管理的挑战。
Moebius syndrome: The challenge of dental management.
机构信息
Department of Maxillofacial Orthopaedics and Orthodontics, Institute of Mother and Child, Warsaw, Poland.
Department and Clinic of Maxillofacial Orthopaedics and Orthodontics of Poznan University of Medical Sciences.
出版信息
Eur J Paediatr Dent. 2019 Jun;20(2):143-146. doi: 10.23804/ejpd.2019.20.02.12.
AIM
Moebius syndrome (MBS) is a rare disorder which involves unilateral or bilateral paralysis or lack of the VI and VII cranial nerves. This is accompanied by abnormalities affecting the head, mouth, upper and lower limbs, and chest. A distinguishing feature of this syndrome is the so-called mask-like face. A small number of publications relating to occlusal and dental bnormalities and documenting the progress of orthodontic treatment has led the authors to present the case of a patient with Moebius syndrome.
CASE REPORT
A patient with Moebius syndrome was initially treated by means of removable appliances and later by means of a fixed appliance after permanent tooth extractions. As a result of the treatment, there was an improvement in the ratio of the posterior facial height to the anterior facial height: Sgo/NGn increased from 55.8% to 59.1%, which is closer to the Caucasian population norm.
CONCLUSION
The aesthetic result was satisfactory both for the patient and for her parents.
目的
Moebius 综合征（MBS）是一种罕见的疾病，涉及单侧或双侧 VI 和 VII 颅神经麻痹或缺失。这伴随着影响头部、口腔、上下肢和胸部的异常。该综合征的一个显著特征是所谓的面具样脸。少数关于咬合和牙齿异常的出版物，并记录了正畸治疗的进展，促使作者提出了 Moebius 综合征患者的病例。
病例报告
Moebius 综合征患者最初通过可摘义齿治疗，然后在拔除恒牙后通过固定义齿治疗。由于治疗，后面高与前面高的比例得到了改善：Sgo/NGn 从 55.8%增加到 59.1%，更接近白种人群的正常值。
结论
患者及其父母对美学效果都很满意。
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