Aneiros Castro Belén, Cano Novillo Indalecio, García Vázquez Araceli, De Miguel Moya Mónica
Pediatric Surgery, Hospital Álvaro Cunqueiro, Vigo, Spain.
Pediatric Surgery, Hospital Universitario 12 de Octubre, Madrid, Spain.
BMJ Case Rep. 2019 Jun 26;12(6):e229986. doi: 10.1136/bcr-2019-229986.
This case report describes an extremely rare association between gallbladder agenesis and choledochal cyst (CC). A 9-year-old girl presented with recurrent abdominal pain in the right upper quadrant. Radiological studies revealed a CC type IVa and an agenesis of gallbladder and cystic duct. Due to the possibility of biliary neoplasm, the patient underwent cyst resection and hepaticoduodenostomy. Histopathological findings showed inflamed fibrous tissue covered by biliary epithelium with no evidence of malignancy.
本病例报告描述了胆囊缺如与胆总管囊肿（CC）之间一种极其罕见的关联。一名9岁女孩出现右上腹反复腹痛。影像学检查显示为IVa型胆总管囊肿以及胆囊和胆囊管缺如。由于存在胆管肿瘤的可能性，该患者接受了囊肿切除术和肝十二指肠吻合术。组织病理学检查结果显示，炎症性纤维组织被胆管上皮覆盖，未发现恶性证据。
