Kozlowski Anna, Murati Michael, Ogilvie Christian, Hess Donavon, Miller Daniel, Hook Kristen
University of North Dakota School of Medicine and Health Sciences, Grand Forks, North Dakota.
Gundersen Health Transitional Year Residency, La Crosse, Wisconsin.
Pediatr Dermatol. 2019 Sep;36(5):677-680. doi: 10.1111/pde.13886. Epub 2019 Jun 27.
Fibrous hamartoma of infancy (FHI) is a benign, poorly demarcated, unencapsulated hamartoma contiguous with surrounding fat. This case highlights pronounced bony remodeling and muscle atrophy associated with FHI in a 6-week-old girl. Emphasis is placed on pathologic diagnosis and mechanisms, treatment considerations, and the multidisciplinary approach utilized in the management of the disorder.
婴儿纤维性错构瘤(FHI)是一种良性、边界不清、无包膜的错构瘤,与周围脂肪相连。本病例突出显示了一名6周龄女童的FHI相关明显骨质重塑和肌肉萎缩。重点在于病理诊断及机制、治疗考量以及该疾病管理中采用的多学科方法。