皮肤结节性淀粉样变：面部的毁容性表现。

Cutaneous Nodular Amyloidosis: A Disfiguring Aspect of the Face.

作者信息

Dupont Letícia, Martins Souza Paulo Ricardo, Damiani Leandro, Boff Ana Letícia

机构信息

Hospital Santa Casa de Misericórdia de Porto Alegre, Porto Alegre, RS, Brazil.

出版信息

Am J Dermatopathol. 2019 Dec;41(12):945-947. doi: 10.1097/DAD.0000000000001470.

DOI:10.1097/DAD.0000000000001470

PMID:31268923

Abstract

Primary localized cutaneous nodular amyloidosis is a rare plasma cell dyscrasia in which an amorphous material consisting of light chain amyloid is produced and deposited in the dermis, with varied clinical presentation. We describe the case with unusual and tumor lush clinical presentation in the face with no progression to systemic disease and no evidence of extracutaneous commitment.

摘要

原发性局限性皮肤结节性淀粉样变性是一种罕见的浆细胞发育异常，其中由轻链淀粉样蛋白组成的无定形物质产生并沉积于真皮，临床表现多样。我们描述了一例面部出现不寻常且肿瘤丰富的临床表现的病例，该病例未进展为全身性疾病，也无皮肤外受累的证据。