Abu-Ghname Amjed, Masoumy Mohamad, Monson Laura A
Division of Plastic Surgery at Texas Children's Hospital/ Michael E. DeBakey, Department of Surgery, Baylor College of Medicine, Houston, TX.
J Craniofac Surg. 2019 Sep;30(6):1866-1868. doi: 10.1097/SCS.0000000000005727.
Pierre Robin sequence is a triad of micrognathia, glossoptosis, and airway obstruction that has reported associations with numerous birth defects and anomalies including craniocervical pathologies. Given the number of airway assessments and neck manipulations these neonates experience, undetected cervical instability can result in detrimental consequences. The authors present a case of a neonate with non-syndromic Pierre Robin sequence planned for mandibular distraction osteogenesis that developed abnormal motor activity following intubation. The patient was eventually diagnosed with cervical spine stenosis and craniocervical instability after radiologic investigation. This paper demonstrates the significance of preoperative cervical spine evaluation and the importance of maintaining high level of suspicion when performing neck manipulations in those high-risk infants.
皮埃尔·罗宾序列征是一种三联征，包括小颌畸形、舌后坠和气道阻塞，据报道与多种出生缺陷和异常有关，包括颅颈疾病。鉴于这些新生儿经历的气道评估和颈部操作的次数，未被发现的颈椎不稳定可能会导致有害后果。作者介绍了一例计划进行下颌骨牵张成骨术的非综合征性皮埃尔·罗宾序列征新生儿病例，该患儿在插管后出现了异常运动活动。经影像学检查，该患者最终被诊断为颈椎管狭窄和颅颈不稳定。本文证明了术前颈椎评估的重要性，以及在对这些高危婴儿进行颈部操作时保持高度怀疑的重要性。
