Lin Yang, Deng Changkai, Peng Qiang
Department of Pediatric Surgery, Chengdu Women's and Children's Central Hospital of Chongqing Medical University, Chengdu, China.
Afr J Paediatr Surg. 2018 Apr-Jun;15(2):63-68. doi: 10.4103/ajps.AJPS_97_17.
Congenital anterior urethrocutaneous fistula (CAUF) is a rare anomaly characterized by fistulization of penile urethra to skin. It's usually seen as an isolated deformity or may accompany genitourinary or anorectal malformations. We aim to define the common properties of patients mentioned in literatures by systematic review. A comprehensive search of PubMed, Embase, Web of Science, and Cochrane Library was performed including cross-referencing independently by two assessors. Selections were restricted to human studies in English. Based on the systematic review, 63 patients in 34 articles were included in the study. Most common fistula site was subcoronal in 29 (46.0%) patients. Chordee was in 8 (14.5%) and associated genitourinary anomaly was detected in 19 (30.2%) of patients. Fistula recurrence ratio was 6/59 (11.3%) using different surgical techniques and 3/6 was closed spontaneously. CAUF is frequently located in subcoronal level and usually an intact urethra distal to it. Success rates are high with the principles of hypospadias surgery.
先天性前尿道皮肤瘘（CAUF）是一种罕见的异常情况，其特征为阴茎尿道与皮肤之间形成瘘管。它通常表现为孤立的畸形，或可能伴有泌尿生殖系统或肛门直肠畸形。我们旨在通过系统评价来明确文献中提及的患者的共同特征。对PubMed、Embase、科学网和考克兰图书馆进行了全面检索，包括由两名评估人员独立交叉引用。纳入的研究仅限于英文的人体研究。基于系统评价，34篇文章中的63例患者被纳入研究。最常见的瘘管部位是冠状沟下，29例（46.0%）患者为此部位。8例（14.5%）患者有阴茎下弯，19例（30.2%）患者检测到相关的泌尿生殖系统异常。采用不同手术技术时，瘘管复发率为6/59（11.3%），其中3/6自发闭合。CAUF常位于冠状沟下水平，其远端尿道通常完整。遵循尿道下裂手术原则，成功率较高。
