Mosa Hazem, Garriboli Massimo
Department of Paediatric Urology, Evelina London Children's Hospital, London, United Kingdom.
European J Pediatr Surg Rep. 2021 Jan;9(1):e9-e12. doi: 10.1055/s-0040-1721469. Epub 2021 Jan 29.
Congenital anterior urethrocutaneous fistula (CAUF) is a rare penile anomaly with only 63 cases reported in the literature. The anomaly can present in isolation or in association with chordee or hypospadias. We report the case of an 8-month-old boy with CAUF that resembles the embryological urethral groove. On examination, a wide urethral groove was noted to cover the midshaft of the penis with a well formed urethra extending proximally and distally and with a normal glandular anatomy, a wide glandular meatus, and a complete foreskin. The urethral groove was tubularized and covered in layers. Surgery was complicated with early superficial skin dehiscence not affecting the urethral repair. Refashioning of the skin was then performed. A satisfactory aesthetic and functional outcome was observed at 7 years' follow-up. Defining the anatomy of CAUF and distal urethra is key in management of these children.
先天性前尿道皮肤瘘（CAUF）是一种罕见的阴茎畸形，文献中仅报道了63例。该畸形可单独出现，也可与阴茎弯曲或尿道下裂合并出现。我们报告了一例8个月大患有CAUF的男孩，其情况类似于胚胎尿道沟。检查时，发现一条宽阔的尿道沟覆盖阴茎中轴，尿道发育良好，向近端和远端延伸，腺体解剖结构正常，尿道口宽阔，包皮完整。尿道沟被管状化并分层覆盖。手术出现早期浅表皮肤裂开的并发症，但未影响尿道修复。随后进行了皮肤重塑。随访7年观察到了满意的美学和功能效果。明确CAUF和远端尿道的解剖结构是治疗这些患儿的关键。
