Jayakumar Naveenkumar, Rathnaprabhu Veerabahu, Ramesh Singaravelu
Department of Oral and Maxillofacial Surgery, Sri Ramachandra Institute of Higher Education and Research, Chennai, Tamil Nadu, India.
Department of Paediatric Dentistry, Kanchi Kamakoti Childs Trust Hospital, Chennai, Tamil Nadu, India.
Ann Maxillofac Surg. 2019 Jan-Jun;9(1):208-210. doi: 10.4103/ams.ams_281_18.
Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment involves surgical resection as primary modality. Prognosis is much better compared to the adult variant with even scope for spontaneous regression following "conservative" resection. We present a case of IFS of the nasomaxillary complex in a 3-month-old female child. We managed our case with surgical resection, and the patient has remained disease free for over 2 years.
婴儿纤维肉瘤(IFS)是一种恶性肿瘤,常见于长骨,2岁以后很少见。在面颌部极为罕见。这种情况常被误诊为畸胎瘤,组织病理学/免疫组织化学检查可确诊。治疗以手术切除为主要方式。与成人型相比,其预后要好得多,甚至在“保守”切除后有自发消退的可能。我们报告一例3个月大女童鼻上颌复合体的婴儿纤维肉瘤病例。我们通过手术切除治疗该病例,患者已无病生存超过2年。