Bots Eva Marianne Theresa, van Wyk Abraham Christoffel, Janson Jacques Teran, Wagenaar Riegardt, Paris Gerald, Koegelenberg Coenraad Frederik Nicolaas
Division of Pulmonology Stellenbosch University Cape Town South Africa.
Pulmonology Department Erasmus Medical Centre Rotterdam the Netherlands.
Respirol Case Rep. 2019 Jul 2;7(7):e00452. doi: 10.1002/rcr2.452. eCollection 2019 Oct.
We present a case of a 34-year-old male who presented with syncope secondary to a large adenoid cystic carcinoma (ACC) of the distal trachea. A computed tomography and flexible bronchoscopy showed almost complete occlusion of the distal trachea. Resection with curative intent was performed, but resection margins were unfortunately not clear. The patient was subsequently offered adjuvant radiotherapy. Tracheal tumours comprise a small proportion of respiratory tract neoplasm, accounting for only about 2% of airway malignancies. Squamous cell carcinoma is the most common tracheal tumour, followed by ACC. Symptoms are usually attributable to the intraluminal component of the tumour causing an obstruction of the airway, resulting in stridor, dyspnoea, wheezing, haemoptysis, and cough. Syncope as a presenting symptom is exceedingly rare.
我们报告一例34岁男性患者，因远端气管巨大腺样囊性癌（ACC）继发晕厥就诊。计算机断层扫描和可弯曲支气管镜检查显示远端气管几乎完全闭塞。进行了根治性切除，但遗憾的是切缘不清晰。随后该患者接受了辅助放疗。气管肿瘤在呼吸道肿瘤中占比小，仅约占气道恶性肿瘤的2%。鳞状细胞癌是最常见的气管肿瘤，其次是腺样囊性癌。症状通常归因于肿瘤的腔内成分导致气道阻塞，从而引起喘鸣、呼吸困难、喘息、咯血和咳嗽。晕厥作为首发症状极为罕见。
