The University of Texas Medical Branch, 301 University Blvd Route 0443, Galveston, TX 77555.
The University of Texas Medical Branch, 301 University Blvd Route 0443, Galveston, TX 77555; Galveston County Medical Examiner's Office, 6607 Hwy 1764, Texas City, TX 77591.
Cardiovasc Pathol. 2019 Sep-Oct;42:54-58. doi: 10.1016/j.carpath.2019.04.002. Epub 2019 May 30.
Kawasaki disease (KD) is among one of the most common causes of vasculitis in children. Since KD was first described in 1967, there have been several reports of patients who did not meet the full diagnostic criteria for KD but who ultimately developed significant coronary artery lesions. Children with incomplete KD are at similar risk of developing coronary artery abnormalities to those with complete Kawasaki. A previously healthy 13-year-old Asian male was seen at a clinic for fever, pharyngitis, and conjunctivitis. He was given antibiotics for a presumed streptococcal pharyngitis. Two weeks later, the decedent complained of chest pain, collapsed, and was transported by Emergency Medical Services to a nearby hospital where he was pronounced deceased on arrival. A complete autopsy was done by the local medical examiner. Histologically, all three coronary arteries showed varying degrees of severe transmural lymphoplasmacytic inflammation, marked vascular smooth muscle intimal proliferation, focal destruction of muscular and elastic layers, and luminal stenosis. Some vessels had recent thrombi. We present an example of incomplete KD in an older child and reiterate the importance of obtaining relevant medical history in sudden death cases that come to the Medical Examiner Office, especially in the pediatric age group.
川崎病 (KD) 是儿童血管炎的最常见病因之一。自 1967 年首次描述 KD 以来,已有几例不符合 KD 全部诊断标准但最终发生严重冠状动脉病变的患者报告。不完全川崎病患儿发生冠状动脉异常的风险与完全川崎病患儿相似。一名之前健康的 13 岁亚裔男性因发热、咽炎和结膜炎到诊所就诊。他因疑似链球菌性咽炎而接受了抗生素治疗。两周后,死者主诉胸痛,晕倒,并由紧急医疗服务机构送往附近医院,在到达时宣布死亡。当地法医进行了全面尸检。组织学上,三条冠状动脉均显示不同程度的严重透壁淋巴浆细胞炎症,明显的血管平滑肌内膜增生,肌层和弹性层局灶性破坏,以及管腔狭窄。一些血管有新鲜血栓。我们展示了一个年龄较大儿童中不完全川崎病的例子,并再次强调在法医办公室遇到的突然死亡病例中获取相关病史的重要性,尤其是在儿科年龄组。