Kothari Shyam S, Relan Jay, Devagourou Velayoudam
Departments of Cardiology, and Cardiothoracic surgery, All India Institute of Medical Sciences, New Delhi, India.
Cardiol Young. 2019 Jul;29(7):986-988. doi: 10.1017/S1047951119001057. Epub 2019 Jul 23.
Patients with a significant left-to-right shunt at ventricular level may become inoperable at an early age due to irreversible pulmonary vascular disease. On the other hand, even suprasystemic pulmonary hypertension due to mitral stenosis remains treatable. We report a 24-year-old patient with large ventricular septal defect, severe mitral stenosis and cyanosis who improved after surgical correction of both the lesions. This emphasises the importance of additional post-capillary pulmonary hypertension in Eisenmenger syndrome.
室水平存在明显左向右分流的患者，可能因不可逆的肺血管疾病在早年就失去手术机会。另一方面，即使是二尖瓣狭窄所致的超系统性肺动脉高压仍可治疗。我们报告了一名24岁的患者，患有大型室间隔缺损、严重二尖瓣狭窄和发绀，在对这两种病变进行手术矫正后病情有所改善。这强调了毛细血管后肺动脉高压在艾森曼格综合征中的重要性。
