Namita U, Rajesh S, Vidya C
Department of Family Medicine, Kerala Institute of Medical Sciences, Trivandrum, Kerala, India.
Department of Rheumatology, Kerala Institute of Medical Sciences, Trivandrum, Kerala, India.
J Family Med Prim Care. 2019 Jun;8(6):2158-2160. doi: 10.4103/jfmpc.jfmpc_281_19.
Eosinophilic fasciitis (EF, also called Shulman syndrome) is a rare connective tissue disorder with poorly understood pathogenesis and unknown etiology. EF is characterized initially by limb or trunk erythema and edema and later by collagenous thickening of the subcutaneous fascia. Here, we present the case of a 16-year-old boy who presented with typical clinical features of EF with a history of typical trigger factor - preceding strenuous physical activity and had a rarer atypical association of hypercalcemia and raised angiotensin converting enzyme (ACE) levels.
嗜酸性筋膜炎(EF,也称为舒尔曼综合征)是一种罕见的结缔组织疾病,其发病机制尚不清楚,病因不明。EF最初的特征是肢体或躯干红斑和水肿,随后是皮下筋膜的胶原增厚。在此,我们报告一例16岁男孩的病例,该男孩具有EF的典型临床特征,有典型的触发因素病史——剧烈体力活动之前,并且存在罕见的非典型关联,即高钙血症和血管紧张素转换酶(ACE)水平升高。