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多形性未分化主动脉肉瘤表现为血管内动脉瘤修复术后持续内漏。

Pleomorphic undifferentiated aortic sarcoma presenting as persistent endoleak after endovascular aneurysm repair.

作者信息

Whittington Eric A, Duncan Lisa D, McNally Michael M

机构信息

Department of Surgery, University of Tennessee Medical Center, Knoxville, Tenn.

Department of Pathology, University of Tennessee Medical Center, Knoxville, Tenn.

出版信息

J Vasc Surg Cases Innov Tech. 2019 Jun 29;5(3):294-297. doi: 10.1016/j.jvscit.2019.04.006. eCollection 2019 Sep.

DOI:10.1016/j.jvscit.2019.04.006
PMID:31334403
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6614707/
Abstract

Sarcomas of the aorta are rare tumors with an unknown incidence and wide variety of clinical presentations. These malignant neoplasms are often manifested in an advanced state and with symptoms of nonmalignant vascular disease owing to a delay in diagnosis. We present the case of a 78-year-old man in whom workup was initially performed for a persistently enlarging abdominal aortic aneurysm after endovascular aortic repair but who was subsequently found to have a pleomorphic undifferentiated sarcoma of the aorta.

摘要

主动脉肉瘤是罕见肿瘤,发病率未知,临床表现多样。这些恶性肿瘤常因诊断延迟而在晚期出现,并伴有非恶性血管疾病的症状。我们报告一例78岁男性患者,最初因血管腔内主动脉修复术后腹主动脉瘤持续增大而进行检查,随后发现患有主动脉多形性未分化肉瘤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/3268fc2976a0/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/2cfd0a8240b7/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/f63cfe677420/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/ebbd817f33b2/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/049479fe0eb1/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/3268fc2976a0/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/2cfd0a8240b7/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/f63cfe677420/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/ebbd817f33b2/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/049479fe0eb1/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fa78/6614707/3268fc2976a0/gr5.jpg

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主动脉肉瘤:极具挑战性的诊断。
BMJ Case Rep. 2023 Sep 20;16(9):e256722. doi: 10.1136/bcr-2023-256722.
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