Suppr超能文献

后颅窝毛细胞型星形细胞瘤致婴儿角弓反张 1 例报告

Posterior fossa pilocytic astrocytoma presenting with opisthotonus in an infant - A case report.

机构信息

University of Queensland School of Medicine, Brisbane, Queensland, Australia.

Department of Neurosurgery, Queensland Children's Hospital, Brisbane, Queensland, Australia.

出版信息

J Clin Neurosci. 2019 Oct;68:338-341. doi: 10.1016/j.jocn.2019.07.052. Epub 2019 Jul 26.

Abstract

Opisthotonus as a presenting feature in neurosurgical patients is rare, with few reports describing such presentations. Only four reports of opisthotonos secondary to posterior fossa mass were identified. An unclear pathophysiology, and broad aetiology contribute to clinical misdirection. While posterior fossa lesions commonly present with signs of raised intracranial pressure, or cerebellar dysfunction, this case describes the presentation of an infant with opisthotonic posturing, ataxia and autonomic dysfunction secondary to a large pilocytic astrocytoma. Despite initial treatment of hydrocephalus, opisthotonus only resolved with complete surgical resection of the posterior fossa mass. At follow-up, the child remains well and without signs of hypertonicity or other signs or symptoms. Presentations involving opisthotonus are rare, and active exclusion of posterior fossa pathology is necessary. In this case, urgent surgical resection allowed for a positive patient outcome. Description of such a case may contribute to understanding of similar presentations in the neurosurgical context.

摘要

术后角弓反张作为神经外科患者的一种表现较为罕见,仅有少数文献描述过此类表现。仅发现了 4 例因后颅窝肿块引起的角弓反张报告。不明确的病理生理学和广泛的病因导致了临床误诊。虽然后颅窝病变通常表现为颅内压升高或小脑功能障碍的迹象,但本例描述了一例婴儿因大型毛细胞星形细胞瘤而出现角弓反张姿势、共济失调和自主神经功能障碍的表现。尽管最初对脑积水进行了治疗,但仅通过完全切除后颅窝肿块才能缓解角弓反张。随访时,患儿情况良好,无张力过高或其他体征或症状。涉及角弓反张的表现较为罕见,需要积极排除后颅窝病变。在本例中,紧急手术切除使患者获得了良好的预后。描述这样一个病例可能有助于理解神经外科环境中的类似表现。

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验