Belczak Sergio Quilici, da Silva Ingredy Tavares, Marques Gustavo Garcia, Copetti Letícia Flores, Stefaniak Vanessa, Quintas Gustavo Gomes, Uchimura Kaique Bernardo
Centro Universitário São Camilo, São Paulo, SP, Brasil.
Instituto de Aprimoramento e Pesquisa em Angiorradiologia e Cirurgia Endovascular - IAPACE, São Paulo, SP, Brasil.
J Vasc Bras. 2019 Jun 8;18:e20180121. doi: 10.1590/1677-5449.180121.
Behçet's disease (BD) is a multisystemic vasculitis of unknown etiology. Cardiovascular involvement has been thoroughly described in the literature and the major cause of death in BD is secondary to aneurysm complications. In this case report, a patient with BD presented with a recurrent abdominal aortic aneurysm, which was corrected using a custom-made endoprosthesis. The optimal treatment for patients with BD remains highly controversial and challenging because of technical difficulties and frequent recurrence. Endovascular intervention seems to be a feasible alternative with considerably less morbidity than conventional surgery.
白塞病(BD)是一种病因不明的多系统血管炎。心血管受累情况在文献中已有详尽描述,BD患者的主要死因是动脉瘤并发症。在本病例报告中,一名BD患者出现复发性腹主动脉瘤,采用定制的腔内修复装置进行了修复。由于技术困难和频繁复发,BD患者的最佳治疗方案仍极具争议且具有挑战性。血管内介入治疗似乎是一种可行的替代方案,其发病率远低于传统手术。