Rare Association Between Atrioventricular Septal Defect and Partial Anomalous Pulmonary Venous Connection.
作者信息
Murakami Alexandre Noboru, Baston Gabriela Guimarães, Cardoso Mariana Ribeiro Rodero, Marchi Carlos Henrique De, Croti Ulisses Alexandre
机构信息
Universidade Estadual de Londrina (UEL) Serviço de Cirurgia Cardíaca do Norte do Paraná Londrina PR Brazil Serviço de Cirurgia Cardíaca do Norte do Paraná, Universidade Estadual de Londrina (UEL), Londrina, PR, Brazil.
Faculdade de Medicina de São José do Rio Preto (FAMERP) Hospital da Criança e Maternidade de São José do Rio Preto (FUNFARME) Pediatric Cardiovascular Surgery Department SP Brazil Pediatric Cardiovascular Surgery Department of Hospital da Criança e Maternidade de São José do Rio Preto (FUNFARME), Faculdade de Medicina de São José do Rio Preto (FAMERP), SP, Brazil.
出版信息
Braz J Cardiovasc Surg. 2019 Dec 1;34(6):765-768. doi: 10.21470/1678-9741-2019-0203.
CLINICAL DATA
Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation.
CHEST RADIOGRAPHY
Demonstrates cardiomegaly and prominent pulmonary vascular markings.
ELECTROCARDIOGRAPHY
Shows right ventricular hypertrophy and left anterior fascicular block.
ECHOCARDIOGRAPHY
Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein.
COMPUTED TOMOGRAPHY ANGIOGRAPHY
This complementary imaging exam was performed to confirm the diagnosis.
DIAGNOSIS
The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated.
OPERATION
The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.
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