Szychta Wojciech, Cerin Gheorghe, Popa Bogdan Adrian, Felice Armienti, Lanzillo Guido, Diena Marco, Opolski Grzegorz
1st Chair and Department of Cardiology, Medical University of Warsaw, Warsaw, Poland.
Cardiology Division in Cardiac Surgery Dept, Policlinic of Monza, San Gaudenzio Clinic, Novara, Italy.
Echocardiography. 2015 Jun;32(6):1040-3. doi: 10.1111/echo.12863. Epub 2015 Jan 21.
Sinus venosus atrial septal defect (SV-ASD) usually coexists with partial anomalous pulmonary vein connection (PAPVC). It is a difficult diagnosis in transthoracic echocardiography (TTE) due to eccentric position of defects. We present a rare case of atypical anatomical variation in PAPVC, which was never described before. Two right pulmonary veins drained into superior vena cava, which overrode SV-ASD and interatrial septum, a third pulmonary vein into the right atrium. Complete diagnosis could not be set after TTE, nor transesophageal echocardiography, whereas angio-CT was finally conclusive. This diagnostic approach allowed the surgical planning.
