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血涂片说明了一切！先天性血栓性血小板减少性紫癜误诊为免疫性血小板减少症的罕见病例。

Blood film says it all! Rare case of congenital TTP misdiagnosed as ITP.

作者信息

Majeed Memon Ayesha, Ali Natasha

机构信息

Assistant Professor Pathology, Dow International Dental College, Dow University of Health Sciences, Karachi, Pakistan.

Associate Professor Department of Pathology & Laboratory Medicine/Oncology, Aga Khan University Karachi, Pakistan.

出版信息

Int J Pediatr Adolesc Med. 2019 Jun;6(2):58-60. doi: 10.1016/j.ijpam.2019.02.005. Epub 2019 Feb 20.

DOI:10.1016/j.ijpam.2019.02.005
PMID:31388548
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6676363/
Abstract

We report a case of a 16-year-old female who presented with bleeding diathesis. Peripheral blood film examination was consistent with microangiopathic hemolytic anemia with 7% fragmented red blood cells. The ADAMTS13 level was 40 ng/ml (reference range: 630-850 ng/ml). She responded to plasma exchange therapy and methylprednisolone and was discharged in a stable condition.

摘要

我们报告一例16岁女性，她表现出出血倾向。外周血涂片检查结果符合微血管病性溶血性贫血，破碎红细胞占7%。ADAMTS13水平为40 ng/ml（参考范围：630 - 850 ng/ml）。她对血浆置换疗法和甲泼尼龙治疗有反应，出院时病情稳定。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/10c9/6676363/945cf26c423b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/10c9/6676363/f82757a339b6/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/10c9/6676363/945cf26c423b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/10c9/6676363/f82757a339b6/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/10c9/6676363/945cf26c423b/gr2.jpg

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Prague Med Rep. 2009;110(3):239-44.
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