de Boer H H, Verbout A J, Nielsen H K, van der Eijken J W
Department of Orthopedics, University Hospital, Leiden, The Netherlands.
Acta Orthop Scand. 1988 Aug;59(4):425-9. doi: 10.3109/17453678809149396.
Four patients with neurofibromatosis and a dysplastic type of congenital pseudarthrosis of the tibia were treated by resection of the lesion and reconstruction of the extremity with a free vascularized fibular graft. Solid union of the graft was achieved within 3 months in 3 children. However, valgus malalignment of the tibia progressed in all 3. One child was treated with resection of a lateral fibrotic band and another with distal tibial epiphysial distraction and realignment. In the fourth patient, who was skeletally mature, a nonunion developed proximally.
4例患有神经纤维瘤病且伴有发育异常型先天性胫骨假关节的患者接受了病变切除,并采用带血管游离腓骨移植进行肢体重建。3例儿童患者在3个月内移植骨实现了牢固愈合。然而,所有3例患者胫骨均出现了外翻畸形。1例患儿接受了外侧纤维化带切除治疗,另1例接受了胫骨远端骨骺牵张和矫正治疗。第4例患者骨骼已成熟,近端出现了骨不连。