Lahiji Farivar A, Asgari Farhang, Mirzaee Fateme, Zafarani Zohreh, Aslani Hamidreza
Shahid Beheshti University of Medical Sciences, Iran.
Lorestan University of Medical Science, Iran.
Int J Surg Case Rep. 2019;61:285-290. doi: 10.1016/j.ijscr.2019.07.076. Epub 2019 Aug 1.
Radial club hand (RCH) is a rare congenital deformity leading in several functional and psychological problems. However, our knowledge about the long-term functional outcomes of treating RCH is limited. In current study, we investigated the outcomes of centralization and pollicization using second or third metacarpal bone in RCH patients.
There were 15 hands (13 patients) with RCH underwent centralization and pollicization using second or third metacarpal bone or tendon transfer. The patients aged 1.2 ± 1 years at the time of the surgery. On early postoperative x-rays, the forearm-hand angle was measured. The patients were followed for 6.2 ± 2.3 years. At the final visit, disabilities of arm, shoulder and hand (DASH) score was completed. Furthermore, forearm-hand angle and range of motion of both wrists in sagittal and coronal planes were measured.
The mean of forearm-hand angle increased significantly. In 11 wrists, forearm-hand angle increased only 10 degrees of less. The range of operated wrist was improved in sagittal and coronal planes. The relative range of wrist motion in patients with unilateral deformity in sagittal and coronal planes was 83 ± 11 percent and 61 ± 12 percent. Three patients developed skin necrosis.
Early centralization and pollicization using second or third metacarpal bone can significantly restore the range of motion and function in patients with RCH.
桡侧多指畸形(RCH)是一种罕见的先天性畸形,会导致多种功能和心理问题。然而,我们对治疗RCH的长期功能结果的了解有限。在本研究中,我们调查了使用第二或第三掌骨对RCH患者进行中心化和拇指化手术的结果。
15只手(13例患者)患有RCH,接受了使用第二或第三掌骨或肌腱转移的中心化和拇指化手术。手术时患者年龄为1.2±1岁。术后早期X线片测量前臂-手角度。对患者进行了6.2±2.3年的随访。在最后一次随访时,完成了手臂、肩部和手部功能障碍(DASH)评分。此外,测量了双腕在矢状面和冠状面的前臂-手角度和活动范围。
前臂-手角度平均值显著增加。11只手腕的前臂-手角度增加不超过10度。手术侧手腕在矢状面和冠状面的活动范围得到改善。单侧畸形患者手腕活动的相对范围在矢状面和冠状面分别为83±11%和61±12%。3例患者出现皮肤坏死。
早期使用第二或第三掌骨进行中心化和拇指化手术可显著恢复RCH患者的活动范围和功能。