Odd-numbered long-chain fatty acid contents in erythrocyte membrane phospholipids in patients with an impaired propionate utilization.

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作者信息

Wendel U, Diekmann E, Laryea M D

机构信息

Metabolic Unit, University Children's Hospital, Düsseldorf, Federal Republic of Germany.

出版信息

J Inherit Metab Dis. 1988;11 Suppl 2:225-8. doi: 10.1007/BF01804242.

DOI:10.1007/BF01804242

PMID:3141708

Abstract

摘要

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引用本文的文献

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本文引用的文献

Propionicacidemia, a new inborn error of metabolism.丙酸血症，一种新的先天性代谢缺陷病。

Pediatr Res. 1968 Nov;2(6):519-24. doi: 10.1203/00006450-196811000-00010.

Branched-chain and odd-numbered fatty acids and aldehydes in the nervous system of a patient with deranged vitamin B 12 metabolism.维生素B12代谢紊乱患者神经系统中的支链脂肪酸、奇数脂肪酸及醛类

J Lipid Res. 1973 Jan;14(1):69-77.

The distribution of 17 carbon fatty acids in the liver of a child with propionicacidaemia.一名丙酸血症患儿肝脏中17碳脂肪酸的分布情况。

Lipids. 1971 Aug;6(8):576-80. doi: 10.1007/BF02531138.

Localisation of enzymic defect in propionicacidaemia.丙酸血症中酶缺陷的定位

Lancet. 1970 May 30;1(7657):1140-3. doi: 10.1016/s0140-6736(70)91216-x.

Analysis of the fatty acid composition of erythrocyte phospholipids by a base catalysed transesterification method--prevention of formation of dimethylacetals.

Clin Chim Acta. 1988 Jan 15;171(1):11-8. doi: 10.1016/0009-8981(88)90286-0.

Methylmalonic and propionic acidemias: lipid profiles of normal and affected human skin fibroblasts incubated with [1-14C]propionate.

Biochem Med Metab Biol. 1986 Jun;35(3):384-98. doi: 10.1016/0885-4505(86)90097-6.

Propionyl-CoA carboxylase deficiency with overflow of metabolites of isoleucine catabolism at all levels.丙酰辅酶A羧化酶缺乏症，伴有异亮氨酸分解代谢各级代谢产物的溢流。

Eur J Pediatr. 1979 Jan 18;130(1):1-14. doi: 10.1007/BF00441893.

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