法布里病中的淋巴结病和肠膀胱瘘

Lymphadenopathy and entero-vesical fistula in Fabry's disease.

作者信息

Carter D, Choi H Y, Telford G, Otterson M, Chitapalli K, Pintar K

机构信息

Department of Pathology, Medical College of Wisconsin, Milwaukee.

出版信息

Am J Clin Pathol. 1988 Dec;90(6):726-31. doi: 10.1093/ajcp/90.6.726.

DOI:10.1093/ajcp/90.6.726

PMID:3143258

Abstract

A case of a 55-year-old man with known Fabry's disease, complicated by entero-vesical fistula and associated with enlarged mesenteric lymph nodes, is reported. Histopathologic and ultrastructural findings of the involved lymph nodes are described, and pathogenesis of the entero-vesical fistula is briefly discussed. This is the first case, to the authors' knowledge, of urologic complication in Fabry's disease.

摘要

报告了一例55岁已知患有法布里病的男性患者，该患者并发肠膀胱瘘并伴有肠系膜淋巴结肿大。描述了受累淋巴结的组织病理学和超微结构 findings，并简要讨论了肠膀胱瘘的发病机制。据作者所知，这是法布里病中首例泌尿系统并发症。