Macey Mathew B, Ho Doreen T, Parres Christopher M, Small Juan E
Department of Neurology, Lahey Hospital and Medical Center, Burlington, MA.
Department of Neurology, Henry Ford Medical Group, Detroit, MI.
J Clin Neuromuscul Dis. 2019 Sep;21(1):47-51. doi: 10.1097/CND.0000000000000243.
Hirayama disease is a rare juvenile amyotrophy that is often misdiagnosed as an unrelated, relentlessly progressive disease. We present the case of an 18-year-old man who presented with weakness and atrophy of the right forearm and hand. Dynamic cervical magnetic resonance imaging was used, revealing the classic findings of epidural venous plexus dilation and anterior displacement of the dural sac. In addition, dilation of the external vertebral venous plexus was visualized. We discuss the clinical utility of dynamic magnetic resonance imaging and the underlying pathophysiology of these findings in Hirayama disease.
平山病是一种罕见的青少年肌萎缩症，常被误诊为一种无关的、进行性疾病。我们报告一例18岁男性病例，该患者表现为右前臂和手部无力及萎缩。采用动态颈椎磁共振成像，显示出硬膜外静脉丛扩张和硬膜囊向前移位的典型表现。此外，还观察到椎外静脉丛扩张。我们讨论了动态磁共振成像的临床应用以及平山病这些表现的潜在病理生理学。
