Umer Masood, Saeed Javeria, Ud Din Nasir, Hilal Kiran
Department of Surgery, Aga Khan University, Karachi, Sindh, Pakistan.
Pathology, Aga Khan University, Karachi, Sindh, Pakistan.
BMJ Case Rep. 2019 Aug 28;12(8):e229371. doi: 10.1136/bcr-2019-229371.
Ossifying fibromyxoid tumour (OFMT) is a rarely occurring soft tissue neoplasm of mesenchymal origin. It is a rarely found tumour with intermediate behaviour and differentiation. Although it is mostly benign, malignant variants also exist. We are presenting a case of 32-year-old man presented in clinic with complaints of painless swelling in left distal thigh. After reviewing his X-ray, a diagnostic biopsy was planned which came out to be suspicious of solitary fibrous tumour. Other radiological workup was done and the patient was planned to undergo wide margin excision. The final histopathology showed a diagnosis of OFMT of soft tissue, atypical variant. The patient is under follow-up and is disease free. This type of tumour possesses potential of local recurrence and metastases; therefore, it is important to keep a long-term follow-up of patient.
骨化性纤维黏液样肿瘤（OFMT）是一种罕见的间叶组织起源的软组织肿瘤。它是一种行为和分化程度中等的罕见肿瘤。虽然它大多为良性，但也存在恶性变体。我们报告一例32岁男性患者，因左大腿远端无痛性肿胀前来就诊。查看其X线片后，计划进行诊断性活检，结果怀疑为孤立性纤维性肿瘤。进行了其他影像学检查，并计划对患者进行广泛边缘切除。最终组织病理学显示诊断为软组织OFMT，非典型变体。该患者正在接受随访，目前无疾病。这种类型的肿瘤具有局部复发和转移的可能性；因此，对患者进行长期随访很重要。
