Sarraj Anas, Duarte Juan, Dominguez Lourdes, Pun Yat-Wah
Department of Cardiovascular Surgery, Hospital Universitario de la Princesa, Diego de León 62, 28006 Madrid, Spain.
Eur J Echocardiogr. 2007 Oct;8(5):384-6. doi: 10.1016/j.euje.2006.04.003. Epub 2006 Jun 8.
The ossifying fibromyxoid tumor (OFMT) of soft parts is a rare soft tissue neoplasm of uncertain lineage. The most common metastases are found in the lung. Herein, we present the first case report of pulmonary metastasis of ossifying fibromyxoid tumor with intracardiac extension, which was resected carefully using cardiopulmonary bypass and cardiac arrest. Subsequently pulmonary left lower lobectomy was performed. The patient recovered uneventfully and was discharged in after a few days. Recently, OFMT has been considered as a tumor of intermediate malignancy. We recommend wide surgical excision of primary tumor and radiotherapy. Early follow-up is mandatory.
软组织骨化性纤维黏液样肿瘤（OFMT）是一种来源不明的罕见软组织肿瘤。最常见的转移部位是肺。在此，我们报告首例伴有心内扩展的骨化性纤维黏液样肿瘤肺转移病例，该病例通过体外循环和心脏停搏进行了仔细切除。随后进行了左肺下叶切除术。患者恢复顺利，数日后出院。最近，OFMT被认为是一种中度恶性肿瘤。我们建议对原发肿瘤进行广泛手术切除并放疗。必须进行早期随访。
