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[经神经活检证实的系统性硬化症伴血管炎相关的多发性单神经病:一例报告]

[Multiple mononeuropathy associated with systemic sclerosis with vasculitis confirmed by nerve biopsy: a case report].

作者信息

Kano Yuya, Kato Hideki, Koike Haruki, Katsuno Masahisa, Oguri Takuya, Yuasa Hiroyuki

机构信息

Department of Neurology, Tosei General Hospital.

Department of Neurology, Nagoya University Graduate School of Medicine.

出版信息

Rinsho Shinkeigaku. 2019 Sep 25;59(9):604-606. doi: 10.5692/clinicalneurol.cn-001320. Epub 2019 Aug 30.

DOI:10.5692/clinicalneurol.cn-001320
PMID:31474645
Abstract

A 68-year-old woman with a medical history of interstitial pneumonia associated with systemic sclerosis (SSc) presented with numbness of the lower limbs and left drop foot. She was diagnosed with multiple mononeuropathy based on the laterality of her symptoms, muscle weakness, thermal hypoalgesia, and nerve conduction study findings. Left sural nerve biopsy showed vasculitis, and steroid therapy was effective. This case highlights the importance of histopathological assessment to select an appropriate treatment strategy.

摘要

一名68岁女性,有与系统性硬化症(SSc)相关的间质性肺炎病史,出现下肢麻木和左足下垂。根据其症状的单侧性、肌肉无力、热觉减退及神经传导研究结果,她被诊断为多灶性单神经病。左侧腓肠神经活检显示血管炎,类固醇治疗有效。该病例强调了组织病理学评估对于选择合适治疗策略的重要性。

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Rinsho Shinkeigaku. 2019 Sep 25;59(9):604-606. doi: 10.5692/clinicalneurol.cn-001320. Epub 2019 Aug 30.
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