Grizelj Ruža, Sindičić Dessardo Nada, Bulić Krešimir, Luetić Tomislav, Mikulić Danko, Antabak Anko, Sjekavica Ivica, Alduk Ana Marija, Konosić Sanja, Režek Tomašić Karolina, Ćaleta Tomislav, Pleško Sanja, Šarić Dalibor, Vuković Jurica
Ruža Grizelj, Department of Pediatrics, University of Zagreb School of Medicine, University Hospital Center Zagreb, Kišpatićeva 12, 10000 Zagreb, Croatia,
Croat Med J. 2019 Aug 31;60(4):301-308. doi: 10.3325/cmj.2019.60.301.
Conjoined twining is a rare medical phenomenon, with an overall prevalence of 1.47 per 100 000 births. This report describes a successful separation of xypho-omphalopagus conjoined twins complicated by unbalanced blood shunting through the porto-systemic anastomoses within the shared liver parenchyma. Significant extrauterine twin-twin transfusion syndrome caused by unbalanced shunting is an extremely rare, and probably under-recognized, hemodynamic complication in conjoined twins necessitating urgent separation. Progressive deterioration with a poor outcome can be prevented if the condition is recognized in a timely manner.
联体双胎是一种罕见的医学现象，总体发生率为每10万例出生中有1.47例。本报告描述了一例剑突-脐部联体双胎成功分离的病例，该病例因共用肝实质内门静脉-体循环吻合处的血流分流不平衡而复杂化。由不平衡分流引起的严重宫外双胎输血综合征是联体双胎中极为罕见且可能未被充分认识的血流动力学并发症，需要紧急分离。如果能及时识别病情，可预防病情进行性恶化及不良后果。
