de Campos Fernando Peixoto Ferraz, da Silva Erasmo Simão, Martines Brenda Margatho Ramos, Martines João Augusto Dos Santos
Department of Internal Medicine - Hospital Universitário - Universidade de São Paulo, São Paulo/SP - Brazil.
Department of Pathology - Faculdade de Medicina - Universidade de São Paulo, São Paulo/SP - Brazil.
Autops Case Rep. 2012 Dec 31;2(4):45-51. doi: 10.4322/acr.2012.032. eCollection 2012 Oct-Dec.
First described in 1936, the diverticulum of Kommerell (DOK) is a dilatation of the proximal segment of an aberrant subclavian artery. Appearing more frequently in the left-sided aortic arch, the aberrant right subclavian artery passes behind the esophagus toward the right arm, causing symptoms in the minority of cases. Diagnosis is generally incidental with this pattern. When symptomatic, dysphagia, respiratory symptoms, hoarseness, chest pain, and upper limb ischemia are the most common complaints. Although debatable, the origin of DOK is accepted as being degenerative or congenital. The degenerative condition is normally associated with atherosclerosis and occurs more frequently after the age of 50 years with no gender predominance. Complications may be life threatening and are more commonly related to the diverticulum aneurysm or when associated with aortic diseases such as aneurysms or dissection. The authors present a case of a 67-year-old male with a history of acute chest pain, neurological disturbances, and hypertensive crisis. The diagnostic workup revealed an aortic arch aneurysm with intramural hematoma and a diverticulum aneurysm of Kommerell. Treatment was conservative at first. The patient presented a satisfactory outcome and was referred to an outpatient clinic for follow up and further therapeutic consolidation.
科默雷尔憩室(DOK)于1936年首次被描述,是异常锁骨下动脉近端段的扩张。异常右锁骨下动脉更常见于左侧主动脉弓,它从食管后方通向右臂,少数情况下会引起症状。这种情况的诊断通常是偶然发现的。出现症状时,吞咽困难、呼吸道症状、声音嘶哑、胸痛和上肢缺血是最常见的主诉。尽管存在争议,但DOK的起源被认为是退行性或先天性的。退行性病变通常与动脉粥样硬化有关,50岁以后更常见,无性别差异。并发症可能危及生命,更常见于憩室动脉瘤或与主动脉疾病如动脉瘤或夹层相关时。作者报告了一例67岁男性病例,有急性胸痛、神经功能障碍和高血压危象病史。诊断检查发现主动脉弓动脉瘤伴壁内血肿和科默雷尔憩室动脉瘤。起初治疗是保守的。患者预后良好,被转诊至门诊进行随访和进一步的治疗巩固。