Kothari Shana, Kalinowski Michael, Shah Natasha, Raddawi Hareth
University of Illinois at Chicago/Advocate Christ Medical Center, Oak Lawn, IL, USA.
Advocate Lutheran General, Park Ridge, IL, USA.
J Investig Med High Impact Case Rep. 2019 Jan-Dec;7:2324709619878337. doi: 10.1177/2324709619878337.
Idiopathic non-cirrhotic portal hypertension is a rare diagnosis caused by an unknown etiology with elevated intrahepatic portal pressures in the absence of underlying liver disease. We present a unique case of a 57-year-old male with a left ventricular assist device and preserved right ventricular function that was found to have an elevated hepatic venous pressure gradient and sequelae of portal hypertension without underlying liver disease. There is limited treatment available as management is primarily aimed toward preventing complications of the disease. This case highlights the need for further investigative research of this disease entity and its pathogenesis.
特发性非肝硬化性门静脉高压是一种罕见的诊断，由未知病因引起，在无潜在肝脏疾病的情况下肝内门静脉压力升高。我们报告了一例独特的病例，一名57岁男性，植入左心室辅助装置且右心室功能保留，发现其肝静脉压力梯度升高且存在门静脉高压后遗症，但无潜在肝脏疾病。由于治疗主要旨在预防该疾病的并发症，可用的治疗方法有限。该病例凸显了对这种疾病实体及其发病机制进行进一步研究的必要性。
