Abdalla Khalid M, Tashtush Nour A, Aleshawi Abdelwahab J, Talahmeh Ghassan, Alawneh Khaled Z
Department of Diagnostic and Interventional Radiology, Faculty of Medicine, Jordan University of Science and Technology, Irbid, 22110, Jordan.
Faculty of Medicine, Jordan University of Science and Technology, Irbid, 22110, Jordan.
Int J Surg Case Rep. 2019;63:122-124. doi: 10.1016/j.ijscr.2019.09.016. Epub 2019 Sep 23.
Primary renal Ewing's sarcoma is a rare tumor with dismal prognosis. The main treatment modality of treatment is surgical excision with adjuvant or neoadjuvant chemotherapy.
We present a case of primary renal EWS in 27-year-old male. He presented to our center complaining of three days history of severe left flank pain associated with nausea and vomiting. Computerized tomography (CT) revealed a 10 × 7 × 6.5 cm left lower pole renal mass. Left radical nephrectomy was performed and revealed a tumor with uniform round to oval nuclei cells. The cells stained strongly positive for CD 99. The diagnosis was established as primary renal Ewing's sarcoma. The patient refused the chemotherapy. Fortunately, he was free of the disease on regular clinical and radiological follow-up, the last follow up was 30 months post-nephrectomy.
This case highlights the importance of proper surgical treatment and its role in the managing this type of malignancy especially in localized disease at presentation.
原发性肾尤文肉瘤是一种罕见肿瘤，预后不佳。主要治疗方式是手术切除并辅以辅助或新辅助化疗。
我们报告一例27岁男性原发性肾尤文肉瘤病例。他因严重左侧腰痛伴恶心呕吐3天前来我院。计算机断层扫描（CT）显示左肾下极有一个10×7×6.5厘米的肿块。实施了左根治性肾切除术，术中发现肿瘤细胞核呈圆形至椭圆形且均匀一致。这些细胞CD99染色呈强阳性。确诊为原发性肾尤文肉瘤。患者拒绝化疗。幸运的是，在定期临床和影像学随访中他未患此病，最后一次随访是在肾切除术后30个月。
本病例突出了恰当手术治疗的重要性及其在这类恶性肿瘤管理中的作用，尤其是对于初诊时局限期的疾病。
