Kang Byung Moo, Youn Sang Min
Department of Neurosurgery, Korea Cancer Center Hospital, Korea Institute of Radiological and Medical Sciences, Seoul, Korea.
Brain Tumor Res Treat. 2019 Oct;7(2):147-150. doi: 10.14791/btrt.2019.7.e40.
Hemangioblastoma (HBL) in the suprasellar region is very rare and a few cases have been reported. Suprasellar HBL without von Hippel-Lindau disease is much rarer. A 76-year old male patient presented progressively deteriorating visual disturbance. MRI demonstrated solid suprasellar mass of 20 mm in diameter, broadly based to planum sphenoidale and diaphragm sella and dural tail sign after the administration of gadolinium diethylene triamine penta-acetic acid (Gd-DTPA). Preoperative diagnosis was meningioma. Total resection of the tumor was not accomplished because of massive hemorrhage, and the histopathologic examination revealed the tumor to be HBL. The visual disturbance of the patient was not improved. The authors reviewed the literature and considered a differential diagnosis of suprasellar tumors and treatment of suprasellar HBL.
鞍上区血管母细胞瘤（HBL）非常罕见，仅有少数病例报道。无冯·希佩尔-林道病的鞍上HBL更为罕见。一名76岁男性患者出现进行性视力障碍。MRI显示鞍上有直径20 mm的实性肿块，广泛附着于蝶骨平台、鞍膈，注射钆喷酸葡胺（Gd-DTPA）后可见硬膜尾征。术前诊断为脑膜瘤。由于大量出血，未能实现肿瘤全切，组织病理学检查显示肿瘤为HBL。患者的视力障碍未得到改善。作者回顾了文献并探讨了鞍上区肿瘤的鉴别诊断及鞍上HBL的治疗。
