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孤立性右心室心肌致密化不全导致室性心动过速和肺栓塞。

Isolated right ventricular noncompaction caused ventricular tachycardia and pulmonary embolism.

机构信息

Department of Geriatrics, First People's Hospital of Yunnan Province, Kunming, China.

Department of Cardiology, First People's Hospital of Yunnan Province, Kunming, China.

出版信息

Ann Noninvasive Electrocardiol. 2020 Sep;25(5):e12731. doi: 10.1111/anec.12731. Epub 2019 Nov 20.

DOI:10.1111/anec.12731
PMID:31746517
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7506999/
Abstract

Isolated ventricular noncompaction is an unclassified cardiomyopathy due to intrauterine arrest of compaction of the loose interwoven meshwork. Its mortality and morbidity are high, including heart failure, thromboembolic events, and ventricular arrhythmias. Isolated right ventricular noncompaction was reported rarely, especially that causes pulmonary embolism and ventricular tachycardia. We describe a case of isolated noncompaction of the right ventricular causing pulmonary embolism and ventricular tachycardia.

摘要

孤立性心室肌致密化不全是一种未分类的心肌病,其病因是胎儿期疏松交织的网架致密化过程停止。该病死亡率和发病率均较高,包括心力衰竭、血栓栓塞事件和室性心律失常。孤立性右心室致密化不全较为罕见,特别是导致肺栓塞和室性心动过速的病例更为罕见。我们描述了 1 例孤立性右心室致密化不全导致肺栓塞和室性心动过速的病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/df868ad016a0/ANEC-25-e12731-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/451ef17db73a/ANEC-25-e12731-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/0bb1f0058a69/ANEC-25-e12731-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/126baca991e9/ANEC-25-e12731-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/df868ad016a0/ANEC-25-e12731-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/451ef17db73a/ANEC-25-e12731-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/0bb1f0058a69/ANEC-25-e12731-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/126baca991e9/ANEC-25-e12731-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/acfe/7506999/df868ad016a0/ANEC-25-e12731-g004.jpg

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引用本文的文献

1
A case report of isolated right ventricular noncompaction with mutation of ACVRL1: a new cause of noncompaction of ventricular myocardium?孤立性右心室心肌致密化不全伴 ACVRL1 突变 1 例报告:心室心肌致密化不全的新病因?
BMC Cardiovasc Disord. 2023 Apr 29;23(1):224. doi: 10.1186/s12872-023-03132-y.

本文引用的文献

1
Noncompaction of the ventricular myocardium.心室心肌致密化不全
Circulation. 2004 Jun 22;109(24):2965-71. doi: 10.1161/01.CIR.0000132478.60674.D0.
2
Isolated ventricular noncompaction is associated with coronary microcirculatory dysfunction.孤立性心室肌致密化不全与冠状动脉微循环功能障碍有关。
J Am Coll Cardiol. 2002 Feb 6;39(3):450-4. doi: 10.1016/s0735-1097(01)01765-x.
3
Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis.34例孤立性左心室心肌致密化不全成人患者的长期随访:一种预后不良的独特心肌病。
J Am Coll Cardiol. 2000 Aug;36(2):493-500. doi: 10.1016/s0735-1097(00)00755-5.