Orzincolo C, Castaldi G, Bariani L, Franceschini F, Corcione S, Scutellari P N
Department of Radiology, St. Anna Hospital, Ferrara, Italy.
Skeletal Radiol. 1988;17(5):344-7. doi: 10.1007/BF00367180.
Solitary or multiple circumscribed osteolytic areas are described in seven patients, selected from 250 patients with homozygous beta-thalassaemia (Cooley's anaemia). On X-ray examinations, these areas appear as purely osteolytic lesions with well-defined margins not associated with sclerosis. The possible mechanisms are discussed.
在从250例纯合子β地中海贫血(库利贫血)患者中挑选出的7例患者中,描述了孤立或多发的局限性骨质溶解区域。在X线检查中,这些区域表现为边界清晰的单纯骨质溶解病变,不伴有硬化。文中讨论了可能的机制。